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Volume 39 #1

Contents

  1. MODERN APPROACHES TO COCHLEAR IMPLANTATION IN INNER EAR ANOMALIES: AUDIOLOGICAL ASPECTS
  2. THE ROLE OF THE ENVELOPE IN THE DISCRIMINATION OF RIPPLED SPECTRA BY LISTENERS WITH DIFFERENT AUDITORY SENSITIVITY
  3. INFLUENCE OF ACOUSTIC BACKGROUND ON THE CHOICE OF VISUAL STIMULI BY CHILDREN OF EARLY PRESCHOOL AGE
  4. TEMPORAL CHARACTERISTICS OF SPEECH IN PATIENTS WITH MODERATELY SEVERE CHRONIC POSTLINGUAL SENSORINEURAL HEARING LOSS WITHOUT THE USE OF HEARING AIDS AND WITH HEARING PROSTHETICS
  5. ON THE ROLE OF THE AUDITORY CRITICAL BANDS IN EFFECTS OF STIMULUS-SPECIFIC ADAPTATION IN THE ACTIVITY OF PRIMARY AUDITORY CORTEX NEURONS IN AWAKE MICE
  6. NICOTINAMIDE-STREPTOZOTOCIN-INDUCED TYPE 2 DIABETES MELLITUS LEADS TO IMPAIRED FUNCTION OF THE MAIN OLFACTORY SYSTEM IN MALE WISTAR RATS
  7. THREE-DIMENSIONAL OBJECT DETECTION BASED ON L-SHAPE MODEL IN AUTONOMOUS MOTION SYSTEMS

MODERN APPROACHES TO COCHLEAR IMPLANTATION IN INNER EAR ANOMALIES: AUDIOLOGICAL ASPECTS

© 2025 N. T. Tunyan, V. E. Kuzovkov, S. V. Levin, E. V. Bychkova

Saint Petersburg Research Institute of Ear, Throat, Nose and Speech, Saint Petersburg, Russia 190013 St. Petersburg, Bronnitskaya st. h.9, Russia
St. Petersburg State University, Medical Institute, Department of Otorhinolaryngology and Ophthalmology, 199106 St. Petersburg, 21st line of V.I., h.8a, Russia
Audiology City Center for children in St. Petersburg, 194356 St. Petersburg, Esenin st., h.26 building 4, Russia

Received 20 Aug 2024

Indications for cochlear implantation are constantly expanding, going beyond severe and complete hearing loss, including patients with unilateral deafness and, recently, with congenital inner ear malformations (Karamert et al., 2022). Among congenital cases of sensorineural hearing loss, inner ear malformations (IEM) account for approximately 20% of cases, with up to 35% of them meeting the criteria for cochlear implantation (Sennaroglu et al., 2017). Due to the wider use of magnetic resonance imaging (MRI) and computerized tomography (CT) scanning of the temporal bone, the population of cochlear implant (CI) recipients among patients with IEM is also expanding, which naturally requires a retrospective assessment of clinical outcomes. At the same time, it is certainly important to evaluate not only the surgical results, which characterize, first of all, the safety of CI in this subgroup of patients, but also audiological outcomes: the degree of restoration of speech and auditory perception, without which it is impossible to get a complete picture of the effectiveness of cochlear implantation. Given the diverse anatomy of the cochlea in IEM, when planning cochlear implantation, determining of the electrode subtype, length and depth of its insertion, as well as the choice between CI or auditory brainstem implantation is of paramount importance not only for the success of the surgical intervention itself, but also for the results of subsequent auditory and speech rehabilitation. The purpose of this review is to analyze actual data about the audiological results assessment of cochlear implantation in patients with congenital IEM compared to patients with normal cochlear anatomy. We tried to identify IEM, in which CI gives the best results, as well as those malformations that require careful planning of surgery, specific selection of the electrode, as well as prevention of possible perioperative complications.

Key words: cochlear implantation, inner ear malformations, a type of electrode grid

DOI: 10.31857/S0235009225010018  EDN: UUXSTK

Cite: Tunyan N. T., Kuzovkov V. E., Levin S. V., Bychkova E. V. Sovremennye podkhody k kokhlearnoi implantatsii pri anomaliyakh vnutrennego ukha: audiologicheskie aspekty [Modern approaches to cochlear implantation in inner ear anomalies: audiological aspects]. Sensornye sistemy [Sensory systems]. 2025. V. 39(1). P. 3–11 (in Russian). doi: 10.31857/S0235009225010018

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